A CASE OF MULTIPLE SOLITARY FIBROUS TUMOR OF THE PLEURA ASSOCIATED WITH SEVERE HYPOGLYCEMIA: DOEGE-POTTER SYNDROME

Ayalew Tezazu Tamire, Yonas A. Teferi, Jacob Schneider, Berhanu Nega

Abstract


Solitary fibrous tumor of the pleura is a rare primary intrathoracic tumor that arises from mesenchymal tissue underlying the mesothelial layer of the pleura. It usually has an indolent clinical course. The hypoglycemia that accompanies SFTP was first described by Doege and Potter independently in 1930, hence the eponym Doege-Potter syndrome. The incidence of Doege-Potter syndromeis reported to be about 4%. In this report, we present a typical case of Doege-Potter syndrome that was cured through complete surgical resection.

 

Keywords: Solitary Fibrous Tumors; Hypoglycemia, Doege-potter syndrome

 

 


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